Link: Successful surgical repair of pentalogy of cantrell at 14 months of age.

Link: http://www.ncbi.nlm.nih.gov/pubmed/24906266

J Coll Physicians Surg Pak. 2014 May;24 Suppl 2:S129-31. doi: 05.2014/JCPSP.S129S131.
Successful surgical repair of pentalogy of cantrell at 14 months of age.
Akhtar K1, Sultan M1, Ahmed W1, Ullah M1, Sadiq N1.
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Abstract
Pentalogy of Cantrell with ectopia cordis is a rare congenital anomaly, first described in 1958 by Cantrell, has a reported incidence of around 5-10 cases per one million live births with wide variety of clinical presentations. We are reporting a child with ectopia cordis along with cleft lower sternum, upper abdominal wall defect, ectopic umbilicus and diaphragmatic defect. Echocardiography in first month of life revealed a restrictive perimembranous ventricular septal defect and a small patent Foramen Ovale, both closed spontaneously in infancy. CT angiography at 10 months of age revealed a defect in the thoracic and abdominal walls along with herniation of left ventricular apex into epigastrium. The two ventriculi formed a tail that looked like a crocodile. This patient underwent surgical correction at our institution at 14 months of age and recovered well with no residual issue.

PMID: 24906266 [PubMed - indexed for MEDLINE]